A Case Report of Hereditary Angioedema: Challenges in Diagnosis and Management

Authors

  • Alvina Widhani Division of Allergy and Clinical Immunology, Department of Internal Medicine, Faculty of Medicine Universitas Indonesia – Cipto Mangunkusumo Hospital, Jakarta, Indonesia
  • Suzy Maria Division of Allergy and Clinical Immunology, Department of Internal Medicine, Faculty of Medicine Universitas Indonesia – Cipto Mangunkusumo Hospital, Jakarta, Indonesia
  • Rifky Yulian Department of Internal Medicine, Faculty of Medicine Universitas Indonesia/Cipto Mangunkusumo Hospital, Jakarta, Indonesia
  • Anshari Saifuddin Hasibuan Division of Allergy and Clinical Immunology, Department of Internal Medicine, Faculty of Medicine Universitas Indonesia – Cipto Mangunkusumo Hospital, Jakarta, Indonesia
  • Sukamto Koesnoe Division of Allergy and Clinical Immunology, Department of Internal Medicine, Faculty of Medicine Universitas Indonesia – Cipto Mangunkusumo Hospital, Jakarta, Indonesia

Keywords:

hereditary, angioedema, diagnosis, management

Abstract

Hereditary angioedema (HAE) is a rare autosomal dominant genetic disorder which causes bradykinin mediated angioedema. Although it can be life threatening, HAE may be underdiagnosed due to a lack of awareness of the disease and limited access to laboratory testing. Here, we report a case of HAE which was diagnosed only after the patient was referred for COVID-19 vaccination even though he had been experiencing recurrent angioedema for the past 30 years. 

References

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Published

2023-07-28

How to Cite

Widhani, A., Maria, S., Yulian, R., Hasibuan, A. S., & Koesnoe, S. (2023). A Case Report of Hereditary Angioedema: Challenges in Diagnosis and Management. Acta Medica Indonesiana, 55(2), 205. Retrieved from https://www.actamedindones.org/index.php/ijim/article/view/2217

Issue

Vol. 55 No. 2 (2023): Acta Medica Indonesiana

Section

CASE REPORT

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