An 18-Year-Old Man with Idiopathic Non-cirrhotic Portal Hypertension

Authors

  • Irene Saveria Department of Internal Medicine, Faculty of Medicine , University of Brawijaya - Saiful Anwar Hospital, Malang, Indonesia.
  • Syifa Mustika Department of Internal Medicine, Faculty of Medicine , University of Brawijaya - Saiful Anwar Hospital, Malang, Indonesia.

Keywords:

non-cirrhotic portal hypertension, hematemesis, rupture variceal esophagus

Abstract

Non-Cirrhotic Portal Hypertension (NCPH) is a rare cause of hematemesis and melena. Like in cirrhotic patient, hematemesis in NCPH patient was caused by rupture of esophageal varices. But unlike in cirrhotic patient, in NCPH there are no sign of liver failure, because liver physiology is still normal. We reported case of male patient with NCPH that had hematemesis because of rupture of esophageal varices.

References

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European Association for Study of the Liver. EASL Clinical Practice Guidelines:Vascular disease of the liver. J Hepatol. 2016;64(1):179-202.

Lee H, Rehman AR, Fiel MI. Idiopathic noncirrhotic nonportal hypertension: An appraisal. J Pathol Trans Med. 2016;50:17-25

Schouten. Idiopathic non-cirrhotic portal hypertension: a review. Orphan J Rare Dis. 2015;10:67.

Goel A, Elias JE, Eapen CE, et al. Idiopathic non-cirrhotic intrahepatic portal hypertension (NCIPH) - Newer insights into pathogenesis and emerging newer treatment options. J Clin Exp Hepatol. 2014; 4(3): 247–256.

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Published

2019-08-05

How to Cite

Saveria, I., & Mustika, S. (2019). An 18-Year-Old Man with Idiopathic Non-cirrhotic Portal Hypertension. Acta Medica Indonesiana, 51(2), 165. Retrieved from https://www.actamedindones.org/index.php/ijim/article/view/270

Issue

Vol. 51 No. 2 (2019): Acta Medica Indonesiana

Section

CASE REPORT

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